It is a very rare occurrence to find a paper looking at NF2 and the auditory system. There seems to only be a couple on NF2 prevalence in the population, so this is unsurprising. As far as I can recall from my student days, it is one of the few incidences where bilateral (acoustic neuromas) vestibular schwannomas are to be considered. Previously known as NF2 type 2, it now has a slightly more specific title of NF2-related schwannomatosis, an autosomal dominant disorder which impacts the likelihood of tumour growth. Arising from the schwann cells in the nerve, most likely in the vestibular branches, this interesting delve into the audiovestibular impact of NF2 is worth a read (even if some of the references date back to 1932) as it re-evaluates the traditional ‘watch and wait’ approach generally considered for vestibular schwannomas.